Double inlet double outlet I-334

3D Model

Specimen with double inlet left ventricle and double outlet right ventricle.

This is a congenital cardiovascular malformation with a univentricular atrioventricular connection wherein both atria connect to a morphologically left ventricle either via two separate atrioventricular valves or a common atrioventricular valve, such that all or nearly all of the total atrioventricular junctional (annular) area is committed to the left ventricular chamber.

In this heart both atria drain into the left ventricle via two seprate atrioventricular valves. There is a small incomplete right ventricle. There is a ventricular septal defect. The pulmonary trunk and aorta both arise from the right ventricle. The aorta is anterior.

IPCCC classification (01.04.04).

Scanned with Revopoint Miraco.